Which of the following is a key feature of Mauriac syndrome?

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Mauriac syndrome is characterized by a specific set of clinical features that occur as a result of poorly controlled diabetes mellitus, particularly in children. A significant hallmark of this condition is severe liver enlargement due to glycogen deposition. In patients with poorly managed diabetes, an excess of blood glucose leads to the liver storing large amounts of glycogen, which can result in hepatomegaly.

This is distinct from other metabolic and hormonal conditions where appetite and blood pressure would not typically present as defining features. High blood sugar levels, while a common concern in diabetes, is more of a consequence of the underlying disease rather than a distinguishing characteristic of Mauriac syndrome itself. Therefore, the key feature that identifies Mauriac syndrome is the pronounced liver enlargement resulting from glycogen accumulation, which is a direct consequence of abnormal glucose metabolism in the setting of chronic diabetes.

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